LMPD Database

LMP001613

UniProt Annotations

Entry Information
Gene Namehydroxyacyl-Coenzyme A dehydrogenase
Protein EntryHCDH_MOUSE
UniProt IDQ61425
SpeciesMouse
Comments
Comment typeDescription
Catalytic Activity(S)-3-hydroxyacyl-CoA + NAD(+) = 3-oxoacyl-CoA + NADH.
FunctionPlays an essential role in the mitochondrial beta- oxidation of short chain fatty acids. Exerts it highest activity toward 3-hydroxybutyryl-CoA.
PathwayLipid metabolism; fatty acid beta-oxidation.
PtmSuccinylation at Lys-81, adjacent to a coenzyme A binding site. Desuccinylated by SIRT5. {ECO:0000269|PubMed:23806337}.
Sequence CautionSequence=BAA06122.1; Type=Erroneous initiation; Evidence={ECO:0000305};
SimilarityBelongs to the 3-hydroxyacyl-CoA dehydrogenase family. {ECO:0000305}.
Subcellular LocationMitochondrion matrix.
SubunitHomodimer. {ECO:0000250}.