LMPD Database

LMP012627

Record overview

LMPD IDLMP012627
Gene ID29711
SpeciesMacaca mulata (Rhesus monkey)
Gene Namebranched chain keto acid dehydrogenase E1, beta polypeptide
Gene SymbolBckdhb
Alternate names2-oxoisovalerate dehydrogenase subunit beta, mitochondrial; BCKDE1B; BCKDH E1-beta; 2-oxoisovalerate dehydrogenase beta subunit; branched chain keto acid dehydrogenase E1 beta; branched-chain alpha-keto acid dehydrogenase E1 component beta chain;
Chromosome8
Map Location8q31
EC Number1.2.4.4
Summaryplays a role in the conversion of 3-methyl-2-oxobutanoate and lipoamide to S-(2-methylpropanoyl)dihydrolipoamide and CO2 [RGD, Feb 2006]
OrthologsView orthologs and multiple alignments for Bckdhb

Proteins

2-oxoisovalerate dehydrogenase subunit beta, mitochondrial precursor
Refseq ID:NP_062140
Protein GI:158749538
UniProt ID:P35738
mRNA ID:NM_019267
Length:390
RefSeq Status:
MAAVAARAGGLLRLGAAGAERRRRGLRCAALVQGFLQPAVDDASQKRRVAHFTFQPDPESLQYGQTQKMNLFQSITSALDNSLAKDPTAVIFGEDVAFGG
VFRCTVGLRDKYGKDRVFNTPLCEQGIVGFGIGIAVTGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGDLFNCGSLTIRAPWGCVGHGALYHSQSPEA
FFAHCPGIKVVIPRSPFQAKGLLLSCIEDKNPCIFFEPKILYRAAVEQVPVEPYKIPLSQAEVIQEGSDVTLVAWGTQVHVIREVASMAQEKLGVSCEVI
DLRTIVPWDVDTVCKSVIKTGRLLISHEAPLTGGFASEISSTVQEECFLNLEAPISRVCGYDTPFPHIFEPFYIPDKWKCYDALRKMINY
 

transit_peptide: 1..48
inference: non-experimental evidence, no additional details recorded
note: Mitochondrion (Potential); propagated from UniProtKB/Swiss-Prot (P35738.3)
calculated_mol_wt: 5033
peptide sequence: 
MAAVAARAGGLLRLGAAGAERRRRGLRCAALVQGFLQPAVDDASQKRR

mat_peptide: 49..390
product: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
experiment: experimental evidence, no additional details recorded
note: propagated from UniProtKB/Swiss-Prot (P35738.3)
calculated_mol_wt: 37809
peptide sequence: 
VAHFTFQPDPESLQYGQTQKMNLFQSITSALDNSLAKDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVFNTPLCEQGIVGFGIGIAVTGATAIAEIQFA
DYIFPAFDQIVNEAAKYRYRSGDLFNCGSLTIRAPWGCVGHGALYHSQSPEAFFAHCPGIKVVIPRSPFQAKGLLLSCIEDKNPCIFFEPKILYRAAVEQ
VPVEPYKIPLSQAEVIQEGSDVTLVAWGTQVHVIREVASMAQEKLGVSCEVIDLRTIVPWDVDTVCKSVIKTGRLLISHEAPLTGGFASEISSTVQEECF
LNLEAPISRVCGYDTPFPHIFEPFYIPDKWKCYDALRKMINY