LMPD Database

LMP006330

UniProt Annotations

Entry Information
Gene Namemethylmalonyl-Coenzyme A mutase
Protein EntryMUTA_MOUSE
UniProt IDP16332
SpeciesMouse
Comments
Comment typeDescription
Catalytic Activity(R)-methylmalonyl-CoA = succinyl-CoA.
CofactorName=adenosylcob(III)alamin; Xref=ChEBI:CHEBI:18408;
FunctionInvolved in the degradation of several amino acids, odd- chain fatty acids and cholesterol via propionyl-CoA to the tricarboxylic acid cycle. {ECO:0000250}.
SimilarityBelongs to the methylmalonyl-CoA mutase family. {ECO:0000305}.
SimilarityContains 1 B12-binding domain. {ECO:0000255|PROSITE- ProRule:PRU00666}.
Subcellular LocationMitochondrion matrix.
SubunitHomodimer.