LMPD Database

LMP006938

Gene Information

Entrez Gene ID851414
Gene Namebiotin--[acetyl-CoA-carboxylase] ligase BPL1
Gene SymbolBPL1
SpeciesSaccharomyces cerevisiae S288c
Gene Ontology (GO Annotations)
GO IDSourceTypeDescription
GO:0005737 IEA:UniProtKB-KWCcytoplasm
GO:0005524 IEA:UniProtKB-KWFATP binding
GO:0004077 IMP:SGDFbiotin-[acetyl-CoA-carboxylase] ligase activity
GO:0004078 IEA:UniProtKB-ECFbiotin-[methylcrotonoyl-CoA-carboxylase] ligase activity
GO:0004079 IEA:UniProtKB-ECFbiotin-[methylmalonyl-CoA-carboxytransferase] ligase activity
GO:0004080 IEA:UniProtKB-ECFbiotin-[propionyl-CoA-carboxylase (ATP-hydrolyzing)] ligase activity
GO:0071734 IDA:SGDFbiotin-[pyruvate-carboxylase] ligase activity
GO:0009305 IDA:SGDPprotein biotinylation
KEGG Pathway Links
KEGG Pathway IDDescription
ko00780Biotin metabolism
sce00780Biotin metabolism
sce01100Metabolic pathways
BIOCYC Pathway Links
BIOCYC Pathway IDDescription
PWY0-1264biotin-carboxyl carrier protein assembly
REACTOME Pathway Links
REACTOME Pathway IDDescription
5618669Biotin transport and metabolism
5618374Defective AMN causes hereditary megaloblastic anemia 1
5618384Defective BTD causes biotidinase deficiency
5618383Defective CD320 causes methylmalonic aciduria
5618375Defective CUBN causes hereditary megaloblastic anemia 1
5618372Defective GIF causes intrinsic factor deficiency
5618386Defective HLCS causes multiple carboxylase deficiency
5618373Defective LMBRD1 causes methylmalonic aciduria and homocystinuria type cblF
5618381Defective MMAA causes methylmalonic aciduria type cblA
5618378Defective MMAB causes methylmalonic aciduria type cblB
5618380Defective MMACHC causes methylmalonic aciduria and homocystinuria type cblC
5618379Defective MMADHC causes methylmalonic aciduria and homocystinuria type cblD
5618377Defective MTR causes methylmalonic aciduria and homocystinuria type cblG
5618376Defective MTRR causes methylmalonic aciduria and homocystinuria type cblE
5618382Defective MUT causes methylmalonic aciduria mut type
5618369Defective TCN2 causes hereditary megaloblastic anemia
5618385Defects in biotin (Btn) metabolism
5618370Defects in cobalamin (B12) metabolism
5618371Defects in vitamin and cofactor metabolism
5618026Disease
5618023Metabolism
5618368Metabolism of vitamins and cofactors
5618367Metabolism of water-soluble vitamins and cofactors