Gene/Proteome Database (LMPD)

LMPD ID
LMP001843
Gene ID
Species
Homo sapiens (Human)
Gene Name
retinaldehyde binding protein 1
Gene Symbol
Synonyms
CRALBP
Alternate Names
retinaldehyde-binding protein 1; cellular retinaldehyde-binding protein; cellular retinaldehyde-binding protein-1
Chromosome
15
Map Location
15q26
Summary
The protein encoded by this gene is a 36-kD water-soluble protein which carries 11-cis-retinaldehyde or 11-cis-retinal as physiologic ligands. It may be a functional component of the visual cycle. Mutations of this gene have been associated with severe rod-cone dystrophy, Bothnia dystrophy (nonsyndromic autosomal recessive retinitis pigmentosa) and retinitis punctata albescens. [provided by RefSeq, Jul 2008]
Orthologs

Proteins

retinaldehyde-binding protein 1
Refseq ID NP_000317
Protein GI 4506541
UniProt ID P12271
mRNA ID NM_000326
Length 317
RefSeq Status REVIEWED
MSEGVGTFRMVPEEEQELRAQLEQLTTKDHGPVFGPCSQLPRHTLQKAKDELNEREETREEAVRELQEMVQAQAASGEELAVAVAERVQEKDSGFFLRFIRARKFNVGRAYELLRGYVNFRLQYPELFDSLSPEAVRCTIEAGYPGVLSSRDKYGRVVMLFNIENWQSQEITFDEILQAYCFILEKLLENEETQINGFCIIENFKGFTMQQAASLRTSDLRKMVDMLQDSFPARFKAIHFIHQPWYFTTTYNVVKPFLKSKLLERVFVHGDDLSGFYQEIDENILPSDFGGTLPKYDGKAVAEQLFGPQAQAENTAF

Gene Information

Entrez Gene ID
Gene Name
retinaldehyde binding protein 1
Gene Symbol
Species
Homo sapiens

Gene Ontology (GO Annotations)

GO ID Source Type Description
GO:0044297 IEA:Ensembl C cell body
GO:0005829 TAS:Reactome C cytosol
GO:0005502 IEA:Ensembl F 11-cis retinal binding
GO:0019841 IEA:UniProtKB-KW F retinol binding
GO:0005215 IEA:InterPro F transporter activity
GO:0007603 TAS:Reactome P phototransduction, visible light
GO:0001523 TAS:Reactome P retinoid metabolic process
GO:0007601 TAS:ProtInc P visual perception
GO:0006776 TAS:ProtInc P vitamin A metabolic process

REACTOME Pathway Links

REACTOME Pathway ID Description
REACT_160156 The canonical retinoid cycle in rods (twilight vision)
REACT_160083 The retinoid cycle in cones (daylight vision)

Domain Information

InterPro Annotations

Accession Description
IPR001251 CRAL-TRIO domain
IPR011074 CRAL/TRIO, N-terminal domain
IPR001071 Cellular retinaldehyde binding/alpha-tocopherol transport

UniProt Annotations

Entry Information

Gene Name
retinaldehyde binding protein 1
Protein Entry
RLBP1_HUMAN
UniProt ID
Species
Human

Comments

Comment Type Description
Disease Bothnia retinal dystrophy (BRD) [MIM
Disease Retinitis pigmentosa autosomal recessive (ARRP) [MIM
Disease Retinitis punctata albescens (RPA) [MIM
Disease Rod-cone dystrophy Newfoundland (NFRCD) [MIM
Function Soluble retinoid carrier essential the proper function of both rod and cone photoreceptors. Participates in the regeneration of active 11-cis-retinol and 11-cis-retinaldehyde, from the inactive 11-trans products of the rhodopsin photocycle and in the de novo synthesis of these retinoids from 11-trans metabolic precursors. The cycling of retinoids between photoreceptor and adjacent pigment epithelium cells is known as the 'visual cycle'.
Similarity Contains 1 CRAL-TRIO domain. {ECO
Subcellular Location Cytoplasm.
Tissue Specificity Retina and pineal gland. Not present in photoreceptor cells but is expressed abundantly in the adjacent retinal pigment epithelium (RPE) and in the Mueller glial cells of the retina.
Web Resource Name=Mutations of the RLBP1 gene; Note=Retina International's Scientific Newsletter; URL="http://www.retina-international.org/files/sci-news/cralbp.htm";

Identical and Related Proteins

Unique RefSeq proteins for LMP001843 (as displayed in Record Overview)

Protein GI Database Accession Length Protein Name
4506541 RefSeq NP_000317 317 retinaldehyde-binding protein 1

Identical Sequences to LMP001843 proteins

Reference Database Accession Length Protein Name
GI:4506541 DBBJ BAG35364.1 317 unnamed protein product [Homo sapiens]
GI:4506541 GenBank ABZ11130.1 317 Sequence 98 from patent US 7309487
GI:4506541 GenBank ACM80429.1 317 Sequence 5927 from patent US 6812339
GI:4506541 GenBank AFK97747.1 317 Sequence 98 from patent US 8158600
GI:4506541 GenBank AIC49594.1 317 RLBP1, partial [synthetic construct]
GI:4506541 PDB 4CIZ 317 Chain A, Crystal Structure Of The Complex Of The Cellular Retinal Binding Protein With 9-cis-retinal

Related Sequences to LMP001843 proteins

Reference Database Accession Length Protein Name
GI:4506541 GenBank ACM84149.1 344 Sequence 9647 from patent US 6812339
GI:4506541 PDB 3HY5 316 Chain A, Crystal Structure Of Cralbp
GI:4506541 RefSeq XP_001166281.2 317 PREDICTED: retinaldehyde-binding protein 1 isoform X1 [Pan troglodytes]
GI:4506541 RefSeq XP_008972121.1 317 PREDICTED: retinaldehyde-binding protein 1 [Pan paniscus]
GI:4506541 RefSeq XP_009428069.1 317 PREDICTED: retinaldehyde-binding protein 1 isoform X1 [Pan troglodytes]
GI:4506541 RefSeq XP_009428070.1 317 PREDICTED: retinaldehyde-binding protein 1 isoform X1 [Pan troglodytes]